Night Blindness:
Can't see when coming in from bright sunlight
Trips over things when light changes or light is dim
Stays near a light in a dark room or at night
Moves a speaker so light falls on face
May express a desire to enter a room before it is darkened (movie theater, etc.)
Avoids conversations in a darkened area
When walking along a road at night, may appear to stagger or lose balance after an oncoming car has passed
Has problems reading under some lights or in dimly lit areas
Glare sensitive:
Squints and shades eyes in bright lights or fluorescent lighting - complains that the light hurts his/her eyes
Likes to wear sunglasses even in buildings, but especially in bright sunlight
Avoids participating in outdoor sports when the sun is very bright
May appear awkward when exiting from the inside to the outside of a building (when faced with bright light)
Needs contrast:
Has difficulty reading light copies or ditto copies
Often spills when pouring liquids
Can't see stars at night
Restricted field:
Startles easily
Seems to hold eyes in a different direction when looking at some things (because of islands of vision)
Turns head while reading across a page
Uses finger to mark place while reading
Can't find small objects that have been dropped
Fails to glance at another person's handwaving from the side
Bumps into people, tables, and chairs
Stumbles on stairs and curbs
Is quiet in a large group or may edge him/herself to one side when placed in a group
Frequently fails to understand or misses groups instruction. Often relies on friends for information
May appear to ignore others standing by his/ her side
Prefers conversation at distances of 4 to 6 ft.
Problems with visual acuity:
Holds book close to eyes, or bends to read
Places face close to desk while writing
Sits near blackboard
Balance problems:
Can't ride a bicycle
Is considered clumsy
Loses balance easily in the dark
Other:
Frequently last in completing group activities
Exhibits symptoms of anxiousness in new areas
Often last to enter the room
May have some repetitive behavior (seems to do the same things in the same ways, or continues to order the same things at lunch)
May choose to stay home alone rather than be faced with the embarrassment of dealing with a new situation in the dark
May appear unconcerned and may fail to fully participate in groups activities
Frequently hesitates at the top or bottom of stairs (for orientation)
Avoids walking or running in unfamiliar areas, especially when there is bright sunlight or when in a darkened area
Appears to be constantly visually scanning a group
Hearing Loss in Usher Syndrome
Type l
Children are born profoundly deaf or with just a little hearing in the low tones at loud levels of sound.
Most but not all state that hearing aids help only a little or not at all.
Some young children are showing benefit from cochlear implants.
Type II
Children are born hard of hearing with a sloping audiogram so hearing high pitches is harder than hearing low tones.
Hearing aids are effective and most children are mainstreamed.
Hearing loss does not change over many years but may go down with noise exposure or with aging.
When vision gets bad, people think they are losing their hearing but, instead, they are losing the ability to lipread.
I ain't a dumb. 
I have Usher/RP too. I take 15,000 vitamin A, Omega 3, 2000, and Lutein 20mg. My eye doctor said it can slow down progression of vision problems as much as 10-20 years in some people. I have been bullied for tripping over stuff and running into stuff. Bullies are IDIOTS, don't let them get you down. So what if we are a little clumsy, there is no need to be ashamed. I am interested in gene therapy too, but I don't think it is being done yet. Good Luck, Nicky
